Ans.188

*Currarino syndrome*
Childhood familial idiopathic osteoarthropathy. Due to mutation in HLXB9 homeobox gene. Currarino syndrome has an autosomal dominant pattern of inheritance.Usually the sacrum is not formed properly, there is a mass in the presacral space in front of the sacrum, and there are malformations of the anus or rectum . It can also cause an anterior meningocele or a presacral teratoma.